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Spinocerebellar Ataxia

A 33 year old man presented with slowly progressive ataxia, slurred speech and nystagmus since childhood.

Show the Cerebellar Atrophy        Show the Pontine Atrophy       Show the Enlarged 4th Ventricle

Axial MRI scan shows severe atrophy of the cerebellum and pons.  This genetic condition, once termed olivopontocerebellar atrophy (OPCA) is now included under the spinocerebellar ataxias (SCA), a large group of inherited disorders characterized by progressive ataxia and brainstem signs.

Revised 04/19/06.
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